Tag Archives: tragedies

condescending twatbags, mental health, narcissists, nostalgia, psychology, Twitter, YouTube

“Don’t make me break my foot off in yo’ ass!”

Years ago, I got hooked on the old comedy show, Mad TV. I still laugh at some of the hilarious and decidedly not politically correct skits and sketches they did on that show. One that is sticking out in my head this morning is “That’s My White Mama”. That sketch was a parody of the 70s sitcom, That’s My Mama, which was about a single Black guy whose “tart tongued and opinionated mother” wanted him to settle down and get married.

That’s My Mama aired 39 episodes from 1974-1975. I was two years old in 1974, and we moved to England in 1975, so I didn’t see the show when it originally aired. I do remember there were reruns in syndication, but I never actually watched more than an episode or two. I probably would have liked it. My mom told me that when I was very young, the only show I liked on TV was Good Times.

An episode of That’s My Mama… I never knew that Ted Lange (aka Isaac the bartender on The Love Boat) was on this show…

I am old enough to remember That’s My Mama, and years ago, I got the joke when comedian Artie Lange created his parody of that show. Again, I didn’t see it when it originally aired, because I was in Armenia. But I saw the reruns.

“Don’t make me break my foot off in yo ass!”
“You don’t want to wake up my mama.”

As I’m thinking about that sketch, I’m also reading about Artie Lange’s life. He’s yet another funny man who’s experienced a lot of sadness and tragedy in his life. It seems like some of the most hilarious people have the saddest real life stories. Lange has struggled with drug addiction, run ins with the police, poor academic performance, mental health issues, physical health issues, and a father who became a quadriplegic after he fell off a ladder and broke his back. It’s amazing that even in the wake of so many personal struggles, Lange was still able to be funny.

Yesterday, I wrote about how Ex has apparently had a very difficult time letting her adult children spread their wings and fly out of the nest. I mentioned how, when younger daughter got married, Ex repeatedly called and texted her during her honeymoon. There younger daughter was, probably doing certain things for the very first time, and Ex was interrupting her with invitations to go swimming and eat pizza. That was just one of many revelations we heard about; there were many others and, of course, I’ve been observing for over 20 years. This is a “mama” who doesn’t want her children to live their own lives on their own terms.

This morning, I noticed that Ex was back on Twitter. Someone was trying to organize a group trip to Scotland for all the Twitter folk who like to watch Outlander. Naturally, Ex, who has made no secret about her “dream” of visiting Scotland, expressed a desire to participate. A bunch of people– mostly women, from what I can see– seem very excited about the prospect of the event.

Ex wrote:

This would really be amazing although I feel like a wallflower already… I think I’d feel like one in person, as well.

Bill told me that he and Ex rarely went to “nice” restaurants, because Ex felt uncomfortable in them. They also couldn’t afford to dine in nice places, because Ex was constantly buying stuff– everything from depression glass to new cars– off of Bill’s single paycheck.

When the organizer said she should “save her pennies” to afford the trip, Ex wrote:

Yes but how many?!?! I’ve got three autistic children and desperately need other things, a computer, a car, acting scholarships for my daughter… how could I possibly?!?!

Um… she has five children, four of whom are legal adults, and two of whom are married, and have their own families in other states. Her youngest is 16 years old. He has severe autism, and obviously needs his mother’s help, which he actually gets from Bill’s older daughter. The other two “autistic children” are adults, and they both function well enough to go to college. One of the “children” she writes of is my husband’s 31 year old older daughter, who is reportedly in graduate school, so Ex can sponge off of her student loans.

I also find it interesting that Ex includes needing “acting scholarships for her daughter (who is supposedly also an autistic ‘child’)” as her responsibility. Especially when we learned that Ex’s eldest child actually won a scholarship to an acting school in New York City, but Ex sabotaged it. Now she wants her youngest daughter to find an acting scholarship in Scotland? What if she actually did find one? Would Ex let her go without trying to fuck the whole thing up for her?

Another poster wrote this:

I hope I can make it. I am still not working. I really want to go. And I haven’t even got my passport yet so that’s gonna take some time being out of work is not fun but my rotator cuff injury dictate what I do at this point.

Seems to me that if this person (who is not Ex) has this many obstacles, she should probably not plan on going and focus on improving her situation so she can make realistic plans. I only included her response, though, because Ex followed up with this comment:

I’m with you! I’m about to have surgery on my ankle/Achilles tendon!! Ugh…

And when I read this, I couldn’t help but remember Artie Lange’s funny parody. I said to Bill, “Does she need surgery because she broke her foot off in one of her children’s asses?” In all seriousness, it doesn’t surprise me to hear that she needs surgery. She broke her foot when she and Bill were married, because she was gardening with bare feet. I’ll bet it’s the same ankle that is causing her issues now.

Ex’s final statement on this event, upon learning that tickets to the event in Scotland were “limited”, was this:

Oh Lordy… tickets limited and everything eh? I’m guessing no room for wallflowers after all?

Hmmm… a ploy for sympathy, perhaps? Or some other “pity play”, as H.G. Tudor would put it?

I suppose I’m glad to read that she’s not making plans to go to Scotland, in spite of having so many needs. In the past, she would have just gone, regardless. One time, she went on a trip to an LDS temple, instead of paying the mortgage on the house that she and Bill once owned, and she eventually let go into foreclosure. She claimed the Lord would provide, as she went to the temple, where she claimed that Heavenly Father would not let her spend her life alone. This was a very typical response she had to any serious responsibility she had– the Lord will provide… or maybe more accurately, someone else can be guilted or suckered into taking care of the problem. It never seems to occur to her that her actions have consequences that affect people far and wide. Her choice to go to the temple, rather than pay her mortgage, helped cause the house to go into foreclosure, which affected Bill, and by proxy, also affected me. And I’ve never even met this bitch in person!

I can see that Ex doesn’t care too much about flying anymore, either. One of the excuses she gave Bill for not allowing us to have visits with his daughters was that she was terrified of letting them fly, due to terrorism and the prospect of them dying in a plane crash. I guess she’s over that fear now, since it no longer suits her purposes. 😉 Of course, the real reason she didn’t want them to visit was because she couldn’t stand to allow them out of her sphere of influence, and she was afraid they might want to live with us instead of her and #3. She couldn’t bear the idea of them bonding with their other parent, and getting a break from her relentless ploys for attention and demands for complete obedience and control.

I realize that Ex is mentally ill, and she has real issues that stem from her own traumas. However, I also know that Ex is fully aware that her behaviors are wrong. How do I know? Because she doesn’t let that extreme “control freak” side of her show on social media. Based on what she puts out for public consumption, she’s a devoted mom, and super friendly and “cool”. If you know the truth about her, though, you realize that this is an elaborate facade, designed to recruit new victims.

It also occurs to me that the person who is organizing this event to allow online friends to meet offline is really opening herself up to potential exploitation. But then, I guess one does that whenever one meets someone in person. You just never know what lurks beneath the surface of a person’s outer layer. By all superficial appearances, Ex is a very “normal” person. But the reality is, she’s anything but normal. She has raised four of her five children to adulthood, but she’s still clinging to them and using them to form an identity. She’d like them to treat her like a child and give her that idyllic childhood era back. But she’d also like to be in charge, call all the shots, make all of the decisions about money, and have the ability to kick people out of the house and lure them back in at will…

Younger daughter briefly mentioned that Ex did kick her out of the house once. But then, when younger daughter got married, she wanted to intrude on her honeymoon and get her and her new husband to move back to where she lives… perhaps even in the same house! All I can think of is that it’s a miracle that younger daughter is so functional and sane, given what she’s been through in her life. She truly is a model of resilience.

Well… I’ve probably gone on enough about this. I never got around to practicing guitar yesterday, so I think I’ll log off and tend to that. Besides… I spend too much time fascinated by Ex. Don’t want her to break her foot off in my ass.

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memories, nostalgia, tragedies, Virginia

German road signs that make me fall down rabbit holes…

A few days ago, when Bill and I were heading home from our trip to the Black Forest, I looked up and noticed a road sign for a town called Hirschberg. Google tells me that Hirschberg is a town in the northwestern part of the German state of Baden-Württemberg (as well as a place in Thuringia). I’ve never been there, and before Monday, I had never noticed that sign. But seeing the name of that town brought back some very old memories from my hometown of Gloucester, Virginia.

This is something I’ve noticed in Europe and the United Kingdom. A lot of the place names here, and in my home state of Virginia, come from surnames. A lot of places in Virginia, especially, are named after places in older establishments. Take, for instance, the town of Kilmarnock, Virginia. It shares that name with a place in Scotland. I guess people from Scotland settled the town in Virginia and named it after their original hometown across the pond. I have to agree, having been to both places, the landscapes are kind of similar.

In any case, when I saw the name Hirschberg, I was immediately reminded of a tragic story from my childhood, over 40 years ago. The date was March 23, 1981. I was eight years old, and a third grader at Botetourt Elementary School. In March 1981, I had only lived in Gloucester for about nine months. My parents bought their business, The Corner Cottage, in the spring of 1980 and we moved to Gloucester on June 21st of that year, the day after my 8th birthday. I experienced quite a culture shock in Gloucester, because we had come from Fairfax, Virginia, which is a MUCH more populated place. And we’d only been in Fairfax for two years; prior to that, we lived on Mildenhall Air Force Base in Suffolk, England. In 1981, I still felt kind of like a foreigner in the United States, having spent three of my conscious years abroad. I wasn’t fitting in very well in Gloucester and, truth be told, I hated it there.

My next sister, Sarah, was sixteen years old on March 23, 1981. She was soon going to be 17 years old, and she attended eleventh grade at Gloucester High School. I would graduate from there myself in 1990. In 1981, 1990 seemed like a million years away. And in 2022, 1990 seems like it was yesterday.

In 1981, the principal at GHS was Mr. Donald W. Hirschberg. I didn’t know anything at all about him, but I do remember Sarah talking about her life at GHS. She probably mentioned the principal, too. She seemed so grown up to me at that time. I remember she was studying French and was even allowed to come to Botetourt to “teach” French to some of the gifted kids. At the time, one of my friends was one of Sarah’s “pupils”.

I don’t think Sarah was at Botetourt on Monday, March 23, 1981, though. That was a day that is still remembered by a lot of my peers because it was the day that Mr. Hirschberg’s wife, Nancy, and their twelve year old daughter, Julie, would die in a horrific car accident. I’m not absolutely certain, but I think another child also died in that crash. I make that assumption because I found a Facebook post about the accident that mentioned another girl who died. Strangely, I don’t remember hearing as much about her.

I was still very new to Gloucester in 1981, so I never had the pleasure of meeting Julie. She was three years older than me, and went to what was then called Gloucester Middle School and later became an elementary school (after I had finished GMS myself). I do remember the accident, though. It happened at a time when Gloucester had very few traffic lights. I know it’s a cliche, but in 1981, that county was still very much covered in farmland. We had a McDonald’s and a Pizza Hut that served the whole county. Gloucester Courthouse, which is about a mile or two from where I lived, had really disgusting water that tasted like sulfur. Our house had well water, which was only marginally better. I remember turning on the taps and seeing rusty water.

I’m not totally sure where the fatal intersection was, but I know I drove past it many times. Route 17 runs from north to south through Gloucester. It’s the main artery through the county, and it’s virtually impossible to avoid driving on it if you’re traveling through Gloucester. I actually think the intersection was one very close to my home. For years, there was nothing but a stop sign there, where people would wait as traffic coming down Route 17 barreled down the highway. Since 1981, the farmland has been turned into a huge Walmart complex. People probably don’t zoom past that intersection anymore, because it’s now heavily moderated by traffic lights. If that wasn’t the intersection, then it was one not far from there, and I would have passed it many times over the 19 years Gloucester was my actual home.

So there I was on Monday, October 3, 2022, speeding down the Autobahn, suddenly remembering Gloucester in the early 80s. I saw that sign for the town of Hirschberg in Germany, and it made me think of twelve year old Julie… a girl I never knew, but heard a lot about when I was growing up. Knowing how Gloucester was in the 80s, I feel very sure we would have probably met at some point. Back then, Gloucester was the kind of place where most people knew each other. I don’t think it’s like that anymore, though. I do still know a lot of people who live there, as a number of my classmates either never left or have returned with their own families.

I got curious about Mr. Hirschberg, too. So I looked him up, and discovered that he died in 1998. He had moved to Poquoson, a city not far from Gloucester, and remarried a woman with the same first name as his late first wife’s. Mr. Hirschberg, at age 61, wasn’t that old when he passed. I wonder if he never got over the grief of that terrible accident. People on Facebook were still discussing it as recently as 2011, with some saying they would never forget that night. A few said it was the first tragedy of their lives, and the first funeral they ever attended. Some said that they still think of Julie and the other girl who died every time they go through that intersection.

I think about the fact that Julie was just three years older than me, and it appears that she was a very popular girl with a lot of promise. She was involved in many community activities and probably would have gone on to live a very productive life. It amazes me that her life ended the way it did– so suddenly, tragically, and randomly, it seems. It could have been any one of us who met that fate. I wonder what she would think about me– someone who never met her, but was one of her contemporaries– thinking and writing about her 41 years after her death, reading about her on the Internet, which didn’t even really exist for regular people back in 1981. I wonder what she would think about people in the “You grew up in Gloucester” Facebook group, still remembering her in 2011 and posting about that dreadful day in March 1981. Julie never experienced Facebook, but I bet she’d know it well if she had lived to see adulthood. I never knew Julie, but I knew a lot of her friends, and they still miss her so many years later. That amazes me.

I haven’t been to Gloucester since 2010, when my mom finally sold the house I grew up in. I was astonished by how different Gloucester was then. It was weird to walk through the house and see things I hadn’t seen since we moved in back in 1980. Our house was old, and kind of weird, so there was a big plumbing pipe coming up through the floor in the tiny room that had served as my bedroom in the early 80s. It had been covered by my twin sized bed for many years. Now it was laid bare, looking as strange as it did in 1980. Even our house is very different now than it was in 1980. My parents doubled its size in 1984, when they added on a new kitchen and a knitting and needlepoint “shop” for my mom to run. My dad had a new custom picture framing “shop” built in 1997, knocking down the weird building that was erected there some decades before. Now, it’s owned by the lady my dad hired in 1989 to help him frame pictures.

Isn’t it funny how the most random things can cause a person to fall down a rabbit hole of memories? Or, at least that’s how it happens for me. I used to wish I was born in 1968, so I could be closer in age to my sisters and have more of a relationship with them. But now I’m glad I was born when I was. I think it was the right time. I don’t know why my mind takes me on these tangential rides, but I have a feeling someone else out there still remembers Julie. I’ll probably be “visited” here by people from Gloucester, who can recall the spring of 1981, too. I am not a Gloucester native, but I know a lot of people are, and they have long memories.

I was pretty fortunate to grow up in Gloucester, even though I hated it in the 80s. My sisters were all Air Force brats, so they were moved constantly. I don’t know if they really feel like they have a “hometown” like I do. They’ve settled in different places, but their childhoods were nomadic. I used to be envious of them, but then I became an Army wife and experienced that lifestyle myself. I think it would have been hard for me as a child. It’s hard as an adult. It’s nice to know that there is a place where people remember me, even if no one in my family lives there anymore. I’m glad to have some roots… although I doubt I’ll be moving back there. I don’t think I fit there anymore. It’s like the old Neil Diamond song, “I Am… I Said”, when he sings:

Well I’m New York City born and raised
But nowadays
I’m lost between two shores
L.A.’s fine, but it ain’t home
New York’s home
But it ain’t mine no more

Yeah. I can relate to that.

Just because it’s a great song that still works in 2022.
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mental health, religion, tragedies

Switzerland and Utah have more in common than beautiful mountain views…

This post has to do with mass suicide. If you think you might be triggered, you might want to move on to your next Internet station.

The New York Times‘ headline said “4 Die After Falling From Balcony in Swiss Resort Town”. I was instantly curious, since I’ve heard the Swiss are even more anal retentive about safety and precision than the Germans are. Before I read the article, I said to Bill, “Someone is going to get sued into oblivion for this.” I said that because the headline made it sound like negligence was involved and I just assumed that a lovely family had plunged to their deaths because a balcony gave way. The strange truth was, this tragedy had nothing to do with a builder’s or safety inspector’s negligence. Apparently, these four people died on purpose. A fifth person remains hospitalized in serious condition.

The small group of people who died yesterday in Montreux, a beautiful resort town in western Switzerland near idyllic Lake Geneva, were not publicly identified in the article. However, the police believe they were French nationals and members of the same family, consisting of a 40 year old man, his 41 year old wife, his wife’s twin sister, and their 8 year old daughter. The couple’s 15 year old son somehow managed to survive the plunge from the seventh floor apartment from which they all apparently jumped.

When the article was published, the police were still trying to determine exactly what led up to the circumstances leading to this family’s fall from their balcony. According to the story, two police officers had knocked on the family’s door at about 7am. The officers were there to give the parents a summons involving the homeschooling of one of the children. Homeschooling is legal in Switzerland, but children who are homeschooled are still required to be routinely monitored by officials to determine their educational progress. When parents are out of touch with officials, police officers are tasked with issuing summonses. Evidently, this family was not allowing their homeschooled child to be checked.

After they knocked on the door, the police officers heard a voice from inside the apartment, asking them to identify themselves. Then, there was silence. As the officers were about to leave the building, a witness had called the police to inform them that people had fallen from a seventh floor balcony. A neighbor of the family’s stated that the family was very “discreet”. That makes me think that there was something weird going on, even before the adults apparently decided that suicide en masse was the answer to their problems.

I read some of the comments regarding this piece, and one lady posted that this story reminded her of an incident that happened in Salt Lake City Utah in 1978. Her comment is below.

This sounds like an instance in the 1970s involving a family who came to be known as “The Leaping Longos” after a mother and her seven children all jumped out of their hotel room window. It turned out that the father had killed himself the day before and their mother forced them all to jump in some weird type of suicide pact. They were practicing their own brand of religion based on the Mormon church and the father was also evading the authorities. 

This family likely all jumped to their deaths as well, but only after the authorities showed up. The authorities were only trying to establish what was happening with the children due to them being home schooled but it is very likely that they had something else to hide. Fortunately one son has survived, and once he’s able to talk about what happened I’m sure the full story will unfold.

The poor kid has become an orphan and I hope he’s able to recover because it would be even more tragic if he’s permanently impaired.

I was around in 1978, but I was a young child at the time. Obviously, I had never heard of the “Leaping Longos” before I read the above comment. I decided to look them up to see if there was any information about this family. Sure enough, I found the story after a couple of minutes of looking. Here’s a link to a 1993 era article by Deseret News about the lone survivor of the Utah incident. In that case, the lone survivor was a fifteen year old girl. Like the rest of her family, Longo changed her name; in the Deseret article she is called Rachel David.

On August 3, 1978, the David family (originally identified as the Longo family) made the bizarre decision to leap from an eleventh floor balcony at the International Dune Hotel in Salt Lake City. The family had been living in the hotel for about a year, when the patriarch, 39 year old Immanuel David (originally named Charles Bruce Longo), committed suicide by carbon monoxide poisoning. Three days after the suicide, 38 year old Rebecca David and her seven children either jumped or were thrown from the balcony. The lone survivor, Rachel, spent many months in a hospital before she was placed in foster care. She was wheelchair bound in 1993, when she was interviewed by the hosts of the television tabloid show, Inside Edition.

In 1993, Rachel David still believed that her father was God and would be returning to Earth. She also said that she had willingly jumped. She also said that she had been trying to follow the suicide order and, as of 1993, had attempted to kill herself many times. Another article, circa 2000, describes the survivor as “brain damaged”. At the time that article was written, Rachel David was still living with “remnants” of the House of David near Denver, Colorado.

Below is a screenshot of a news article that was written in 1978, just after this event took place.

Freaky story… I wonder if this French family was involved in a similar cult.

And here is a broadcast news item about the 1978 Utah incident…

I can’t even imagine how horrifying this was to witness…

Why do these culty types always gravitate to the name “Immanuel”? Especially when they have ties to Mormonism? According to the news report, David was an excommunicated member of the LDS church. The father was not employed at the time of his death, although according to the video, the bill for the $95 a day was paid on time and in cash, usually with $100 bills. The news story is astonishing, as the physician is very openly talking about the surviving girl’s injuries. We didn’t have HIPAA in those days.

As I listen to this surprisingly lengthy report, I’m confused by the discrepancies in the people’s names. According to the news article, the father’s name was Charles Bruce Longo, but this news report refers to him as Bruce David Longo. And then he changed his name, and all of the names of his wife and children were changed.

As for the French family in Switzerland, slightly more news has emerged about their apparently sudden and bizarre exit from Earth. Apparently, the mother in the French family was a dentist who had worked in Paris. Her sister was an ophthalmologist. The father worked at home. The family had been living in Switzerland for some time, and had residence status. The Daily Mail offers an article with some rather salacious details omitted from the more respectable newspaper articles. Apparently, the family used incense a lot, and ordered many packages. It will be interesting to learn more about why this tragedy occurred, and if this family has anything else in common with the “Leaping Longos” of Salt Lake City.

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ethics, healthcare, memories, Neighbors

Repost: Perpetuating the genetic nightmare…

I am reposting this piece from August 30, 2017, because it goes with the book review I reposted today. It appears as/is. Special thanks to Leevan Jackson who made the featured photo available through Creative Commons.

I have written a few times about my childhood neighbors, people who lived across the dirt road from us in Virginia.  In 1980, when we moved to Gloucester, they were a family of four.  There was a mother, father, brother and sister.  The father did not live at home.  He was in his early 30s and lived at the local psychiatric hospital in Williamsburg because he was suffering from Huntington’s Disease.   The mother was raising her children, twelve year old Michael and nine year old Leslie, by herself. 

In 1980, Michael was also suffering from Huntington’s Disease, having inherited the defective gene and developed the disease much earlier than most people with Huntington’s Disease do.  He died in 1982.  His and Leslie’s father died a couple of years after that.

I was eight in 1980.  I met all of these people when I was a child.  Leslie’s mother worked for my dad for several years until Leslie’s paternal grandmother died and Leslie’s mom inherited some money.  Leslie’s mom bought her own picture framing business and competed against my dad.  The business eventually failed.

Leslie and I weren’t close friends, but we did grow up together.  My parents included Leslie and her mom on a couple of family trips.  In 1985, I remember we all went to Kitty Hawk, North Carolina together.  I seem to remember Leslie and her mom coming with us to Natural Bridge, Virginia once, too.  I grew up waiting for the bus with Leslie and used to dog sit for her mom when they’d take trips to the Smoky Mountains.  Leslie was bright and talented and probably could have done some great things had she not been doomed to get Huntington’s Disease while still fairly young.

Leslie died in 2010, having battled the disease for several years.  She was 39 years old.  She’d given birth to three kids.  One of them died in a freak accident in 1995.  Leslie’s little daughter, just two years old, was accidentally run over by Leslie at the local Walmart.  For some reason, Leslie had allowed the little girl to stand up behind the driver’s seat.  If I recall correctly, she was just coasting forward to the drink machines and, for whatever reason, decided not to put the kid in a car seat.  Leslie had inexplicably left the car door open and the girl fell out and ended up under the car’s tires.  Her older child, then just three years old, was also there.  In 2012, when he was 21 years old, that child would also die in a car accident.  I have to wonder if the accident was really an accident or if the young man had started getting symptoms of Huntington’s Disease and decided to commit suicide. 

In 1996, Leslie had her third child, another son.  He is the only one of her children still living.  I have never met Leslie’s youngest child, but I know his family well.  I also know his dad, since he was in my class in school.  In the 80s, Gloucester was the kind of place where everyone knew each other.  I also knew of Leslie’s older son’s family, since his grandmother used to clean my parents’ house. 

Last night, I decided to look up Leslie’s sole surviving son.  I see that he recently became a father.  I have to wonder how much exposure he got to his mother when she was sick.  I didn’t see Leslie during those years because I left our hometown, but I do remember meeting her father and seeing her brother on a daily basis.  I remember what Huntington’s Disease looked like at an advanced stage.  It’s absolutely devastating.   

I just started reading a book about a woman who married into a family with the Huntington’s Disease gene.  The woman fell in love with her husband before he knew his mother had Huntington’s Disease.  She was dating him when he and his three older sisters found out why their mother wasn’t around when they were growing up.  She’d been in a psychiatric hospital.  The family patriarch wasn’t much of a father figure, so it was left up to the eldest daughter to take care of everyone.  Somehow, the four kids grew up not knowing that their mother had a genetic disorder.  I’m probably halfway through the book so far… The author decided to play the odds and have a son with her husband.

I learned in the book I’m reading that famed songwriter, Woody Guthrie, had Huntington’s Disease.  He had eight children, five of whom died young.  His second of three wives, Marjorie Guthrie, started what would eventually become the Huntington’s Disease Society of America.  Marjorie had four children with Woody, including famous singer-songwriter Arlo Guthrie.  Woody was married to his third wife for just a year before they split; he died in 1967 at age 55.  Woody was never really treated for his disease.  People thought he had schizophrenia or was an alcoholic, due to the extreme mood swings the disease caused.  Because he was famous, his death brought awareness to Huntington’s Disease.  It looks like Arlo and two siblings have escaped their father’s fate.  Today, I very much enjoy listening to music by Arlo’s daughter, Cathy, who plays ukulele in the duo, Folk Uke, with Amy Nelson (Willie Nelson’s daughter).

One of Woody Guthrie’s most famous songs…
Arlo Guthrie performs “Alice’s Restaurant”…
Cathy Guthrie and Amy Nelson performing as Folk Uke.

Every child who has a parent with Huntington’s Disease has a fifty percent chance of developing the disease.  Huntington’s Disease, although genetically perpetuated, is not like cystic fibrosis.  With CF, both parents must have the genetic defect.  Even then, a child born to parents carrying the CF gene has a one in four chance of getting cystic fibrosis, a one in four chance of being clear of the gene, and a two in four chance of being a carrier.  With Huntington’s Disease, it’s a one in two chance.  And if you have the gene, you will get the disease and likely die from it.  There is no treatment or cure for Huntington’s Disease.

A few months ago, I wrote a post about the ethics of knowingly passing along defective genes.  That post was inspired by Zach and Tori Roloff, stars of the TLC show Little People Big World.  They’d just had a baby and some people were saying that they shouldn’t have, since Zach has achondoplasia. Their son, Jackson, also has achondoplasia, which is a type of dwarfism.  For the record, I will say that dwarfism is not quite the same thing as something like CF or Huntington’s Disease.  A person who has achondoplasia can be basically healthy, though abnormally short.  CF and Huntington’s Disease are very serious and debilitating.

I think Huntington’s Disease, in some ways, is crueler than CF is.  Many people with CF are sick from babyhood.  They grow up sick, although some sufferers are much sicker than others.  They often know from a young age whether or not they will be affected by CF. 

A person with a family history of Huntington’s Disease can start life completely normal and not get sick until they’re approaching middle age.  They can develop lives, start families, have careers, and ultimately be stricken by a disease that makes them lose control of their bodies and their minds.  People with Huntington’s Disease grow up wondering if and when it will strike and whether or not they should get tested for the gene.  If they get tested, the news could be good.  They might not have the gene.  Or it can be bad; they have the gene and will eventually get very sick and probably die young.

Leslie’s family was devastated by Huntington’s Disease.  It seemed the gene in her family was worse than some others.  I remember hearing that her grandfather, whom I never met, had the disease.  He’d been adopted and never knew he had a genetic anomaly, so he and his wife, Vashti (whom I did meet), had a family.  I know that besides Leslie’s dad, at least one other sibling got the disease and died young.

I remember my mom telling me, quite emotionally, that Leslie’s mother should have had her daughter’s tubes tied when she was a baby.  I explained to my very practical mom that it would have been unethical to tie Leslie’s tubes.  What if she had been born clear of the gene?  There was a fifty percent chance that she had the defect, but there was also a fifty percent chance she didn’t.  She could have lived a completely normal life.  In 1971, when Leslie was born, I doubt the technology was there to know.  By the time genetic testing was available, I’m sure Leslie didn’t want to know.

I wish Leslie’s grandson much luck.  I truly hope he isn’t going to be afflicted by this terrible disease.  Life is a crap shoot.  He has an aunt and uncle who may or may not have had the genes for Huntington’s Disease and still died very young.  Not having the misfortune of being burdened by a genetically passed disease myself, I can’t even know what it’s like to live with the knowledge that I’m doomed.  Hopefully, Leslie’s son and grandson have escaped Huntington’s Disease.  That disease is a fate I would not wish on my worst enemy.  On the other hand, if Woody Guthrie hadn’t had children, we would be missing out on some great music.

I’ll write a review of the book when I’m finished with it.  It’s amazing what provides food for thought…  And it’s also crazy that I know so much about someone I’ve never met.  It’s not the first time this has happened, either. 

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